Xanuunada Myeloproliferative (MPN), oo hore loo yiraahdo 'myeloproliferative', ayaa ah koox ka mid ah cudurrada ay ka mid yihiin in ka badan hal ama in ka badan oo ah unugyada dhiigga (unugyada dhiigga cad, unugyada dhiigga cas, iyo / ama platelets). Inkasta oo aad la xiriiri kartid ereyga neoplasmka leh kansarka, ma aha in la gooyo cad.
Neoplasm waxaa lagu qeexay koritaan aan caadi ahayn ee unugyada oo sababay isbeddel, waxaana loo kala saari karaa mid aan wanaagsaneyn (kansar aan lahayn), kansar ka hor, ama kansar (malignant).
Marka la eego cudurka, neoplasmalliamka badankood wuxuu kudhicaa laakiin wakhti dheer ayaa laga yaabaa in uu ku dhaco cudurka kansarka (kansarka). Khatarta ah in uu ku dhaco kansarka qaba ciladahaan ayaa hoosta ka xariiqaya muhiimada ay leedahay in lala socdo dabagalka maqaarkaaga.
Qeybaha kala duwan ee miyir-qabadlayaashu waxay is bedeleen sannadihii la soo dhaafay laakiin waxaan dib u eegi doonaa qaybaha guud ee halkan.
Noocyada Myeloproliferative Classic
Noocyada 'classic' myeloproliferative neoplasms waxaa ka mid ah:
- Daawada Polycythemia Vera (PV): Natiijada PV waxay ka timaadaa isbeddellada hidde-keena taas oo keenta kororka unugyada dhiigga cas. Mararka qaarkood unugyada dhiigga cad iyo taranka dhiigga ayaa sidoo kale sarreeya. Korodhka dhiigga ee tirinta dhiigga wuxuu kordhiyaa halista inaad sameysid xinjir dhiig. Haddii lagugu ogaado PV, waxaad leedahay fursad yar oo lagu kobcin karo myelofibrois ama kansar.
- Trombositemia Essential (ET): Isbeddellada hidde-wade ee ET waxay sababtaa in ka badan oo dheellitirma qumman. Tirada korodhka taranka ee kor u kaca waxay kordhineysaa halista xinjirta dhiigga. Khatarta aad ugu jirto inaad qaaddo kansar marka lagugu ogaado ET waa mid aad u yar. ET waa mid u gaar ah MPNs sababtoo ah waxay tahay ogaansho ka saarid. Taasi macnaheedu waa dhakhtarkaaga ayaa ka talaabaya sababaha kale ee tirakoobka ( trombocytosis ) oo ay ku jiraan MPN kale.
- Qaybta Myelofibroxis (PMF): Qaliinka myelofibroxis hore waxaa loo yaqaan 'idiopathic myelofibroxis' ama 'metablasia' agnogenic myeloid. Isbeddelka hidde-ku-galka ee PMF wuxuu ku dhacaa iskudhaf (fibrosis) ee dhuuxa lafta. Nabaradaasi waxay ka dhigeysaa in ay adagtahay dhuuxa lafahaaga si aad u sameysid unugyada cusub ee dhiigga. Taas bedelkeeda PV, PMF guud ahaan waxay keenaysaa dhiig-yarida (tirakoobka dhiigga ee hooseeya). Tirada unugyada dhiigga cad iyo tirakoobka dhiigga ayaa la kordhin karaa ama la yarayn karaa.
- Cudurka Myeloid Leukemia (CML) : CML waxaa sidoo kale loo yaqaannaa 'leukemia leukemia' oo joogto ah. Natiijooyinka CML ee laga helay mutacal hiddo-yaqaan loo yaqaan BCR / ABL1. Isbedelkan wuxuu keenaa kororka granulocytes, nooca unugyada dhiigga cad. Ugu horreyn, waxaa laga yaabaa inaadan lahayn wax astaamo ah oo CML waxaa badanaa lagu helaa dhacdooyinka shaybaarka caadiga ah.
Noocyada Myeloproliferative Neoplasms
"Neeflasmaal" ee "myypoproliferative neoplasms" waxaa ka mid ah:
- Dhallaanka 'Myleomonocyic Leukemia' (JMML): JMML waxaa loo isticmaalaa in lagu magacaabo CML da 'yaryar. Waa nooc naadir ah oo leetemia ah oo ka dhacda dhalaanka iyo ilmanimada hore. Lafaha lafaha ayaa ka badinaya unugyada dhiigga ee myeloid, gaar ahaan mid loogu yeero monocyte (monocytosis). Carruurta leh nooca neurofibromatosis nooca I iyo Noonan syndrome waxay halis weyn ugu jiraan inay horumariyaan JMML marka loo eego carruurta aan lahayn xaaladdan hidda-socodka.
- Cudurka neutrophilic joogtada ah: Cudurka 'neutrophilic leukemia' waa xummad naadir ah oo lagu garto kororka nutrophils, nooc unugyada dhiigga cad. Unugyadaasi waxay markaa ku dili karaan unugyadaada waxana ay sababi karaan beerka iyo beeryarada (hepatosplenomegaly).
- Cudurka Eosinophilic Leukemia / Hypereosinophilic Syndromes (HES): Cudurka eosinophilic leukemia iyo hypereosinophilc syndromes wuxuu u taagan yahay koox cudur ah kuwaas oo lagu garto tirada korodhka eosinophilia (eosinophilia) taas oo keenta dhaawac xagga xubnaha kala duwan. Dad tiro badan oo HES ah ayaa u dhaqma sida finanka myleoproliferative (markaa magaca leetemia eoninophilic joogto ah).
- Cudurka Cudurka Mastarka: Nidaamka (macnaha guud ee jirka oo dhan) Cudurka unugyada mastoolada ama mastosostosis waa miisaan cusub oo cusub oo ku xiran qaybta maaddada 'myeloprolative neoplasms'. Cudurrada unugyada mastuurku waxay ka yimaadaan kor u kaca unugyada mastarada, nooc ka mid ah unugyada dhiigga cad, taas oo markaa soo galeysa dhuuxa lafta, mareenka caloosha, maqaarka, beeryarada iyo beerka. Tani waxay ka duwan tahay mastosytosis cutane oo kaliya saameysa maqaarka. Unugyada mastu waxay sii daayaan histamine taasoo keentay fal-celinta nooca xasaasiyadda ee xasaasiyadda.
Ilaha:
Roufosse F, Klion AD iyo Weller PF. Xanuunada hypereosinophilic: Calaamadaha caafimaadka, cudurka nafsaaniga, iyo baaritaanka. In: UpToDate, Post TW (Ed), UpToDate, Waltham, MA. (Lagu heley 27 Juun, 2016.)
Teferri A. Guudmarka neoplasmallka myeloprolifer. In: UpToDate, Post TW (Ed), UpToDate, Waltham, MA. (Lagu heley 26 Juun, 2016.)
Van Eatton RA. Calaamadaha cudurka iyo cudurka qaaxada ee 'myeloid leukemia'. In: UpToDate, Post TW (Ed), UpToDate, Waltham, MA. (Lagu heley Juun 28, 2016.)