Maxay tahay Pierre Robin?

Isreebreebka Pierre Robin (ama cilladda) waa xaalad dhalan oo keenta isku darka soo socda kuwaas oo ku jira xilliga dhalashada:

Dhibaatooyinkaas oo kale waqtiga dhalashada waxay badanaa keenaan dhibaatooyinka hadalka ee carruurta leh calaamadaha Pierre Robin. 10-85 boqolkiiba kiisaska kale ee calaamadaha nidaamka ayaa dhici kara oo ay ku jiraan:

Dhacdooyinka isbarbardhigga Pierre Robin waa qiyaastii 1 ee 8500 dhalasho, oo saameeya labka iyo dheddigga. Isku xirka Pierre Robin wuxuu ku dhici karaa oo kaliya, laakiin wuxuu la xiriiraa dhowr xaaladood oo kale oo hidde ah sida: Stickler syndrome, Calaamadaha 'CHARGE', 'Shprintzen syndrom', Mobius syndrome, Trisomy 18 syndrome, Trisomy 11q syndrome, ciribtirka 4q syndrome, iyo kuwa kale.

Waxaa jira saddex aragti oo ku saabsan sababta sababa Pierre Robin. Marka ugu horeysa waa in hypoplasia mandibular ay dhacdaa inta lagu jiro toddobaadka 7-aad ee uurka. Tani waxay keenaysaa in carrabka ka maqan yahay xaydhka afka oo ka hortagaya xiritaanka qalabka isgoysyada cagaarka ah oo keenaya lakabka taranka ee U-qaabeeya. Qadar yar oo dheecaan amniotic ah ayaa noqon kara arrin.

Fikradda labaad waxay tahay in dib u dhac ku yimaado horumarinta dareemayaasha ee jilicsanaanta carrabka, tiirarka barbaarinta, iyo faleemada oo ay weheliso daahitaan ku saabsan wareegga dareemaha ee dareemayaasha. Sheekadani waxay sharraxaysaa sababta calaamado badani u xaliyaan qiyaastii 6 sano.

Qodobka seddexaad ayaa ah in dhibaatada ugu weyn ay dhacdaa inta lagu jiro horumarka taas oo keenta xinjirta rhombencephalus (hindbrain - qaybta maskaxda ee ku jirta maskaxda iyo cerebellum).

Ma jiraan wax daawo ah oo loo yaqaan 'Pierre Robin'. Maareynta xaaladda waxay ku lug leedahay daaweynta calaamadaha shakhsiga. Kiisaska intooda badan daanka hoose ayaa si dhaqso ah u koraaya inta lagu jiro sanad-nololeedka ugu horreeya ee nolosha waxayna badanaa u muuqdaan kuwo caadi ah xannaanada. Korniinka dabiiciga ah wuxuu sidoo kale daaweeyaa dhibaatooyinka hawo-mareenka (airway) ee laga yaabo inuu joogo. Mararka qaarkood hawo-mareenka (sida nasophargyngeal ama airway airway) wuxuu u baahan yahay in la isticmaalo muddo wakhti ah. Dhallaanka haweenta waa inuu hagaajiyaa qalliinka maxaa yeelay wuxuu sababi karaa dhibaatooyin quudinta ama neefsashada. Carruur badan oo leh isugeyn Pierre Robin waxay u baahan tahay daaweynta hadalka.

Xiisadda Pierre Robin ee aadka u kala duwan ayaa u dhexeeysa shakhsiyaadka qaarkood maadaama ay dadku leeyihiin kaliya dhowr calaamadood oo la xariira xaaladan, halka kuwa kalena ay yeelan karaan astaamo badan.

Calaamadaha wadnaha iyo xididada ayaa sidoo kale adkaan karta in la maareeyo marka la barbar dhigo qaar ka mid ah cilladaha muruqa ah ee la xidhiidha isdaba-marinta Pierre Robin. Daraasaduhu waxay muujiyeen in isxilqaamiye Pierre Robin, (marka xaaladdu ay dhacdo iyada oo aan jirin cillad kale oo la xidhiidha), had iyo jeer ma kordhiso khatarta dhimashada, gaar ahaan marka dhibaatooyinka nidaamka dareen-wadeyaasha aan la joogin.

> Ilo:

> Xirmada Palat Foundation. Pierre Robin Sequence. http://www.cleftline.org/parents-individuals/publications/pierre-robin-sequence/

> Medline Plus. Tirada Pierre Robin. https://www.nlm.nih.gov/medlineplus/ency/article/001607.htm

> Daaweynta Caawinta. Pierre Robin Syndrome. http://emedicine.medscape.com/article/844143-overview#a4