POEMS syndrome waa cudur dhiig ah oo saameeya qaybo badan oo jirka ka mid ah wuxuuna keenaa calaamado badan. Waxay ragga iyo haweenkuba saameeyaan waxayna badanaa bilaabaan marka ay gaaraan 50 jir, inkastoo ay dhici karto da 'kasta. Lama garanayo sida dhabta ah inta jeer ee cudurka POEMS uu dhaco maxaa yeelay way adag tahay in si sax ah loo baaro. Sababta lama oga.
Astaamaha
POEMS-gaaban waxa ay u taagan tahay:
- P - polyneuropathy, oo macnaheedu yahay astaamaha dareenka sida kabuubyo, xatooyo, iyo / ama daciifnimo gacmaha iyo cagaha
- O - organomegaly, oo macneheedu yahay xubno ballaaran, inta badan beerka, caleemaha, ama qanjidhada. Ilaa boqolkiiba 15 dadka qaba cudurka POEMS waxay qabaan cudurka Castleman (xanuunka lafdhabarta).
- E - endocrinopathy, taasoo macnaheedu yahay isbeddelada soo saarka hoormoonka. Calaamadaha sida sonkorowga , kacsanaanta , joojinta caadada ( amenorrhea ), heerarka tir tirka yar (hypothyroidism), iyo / ama horumarinta naaska ee ragga (ginecomastia) ayaa laga yaabaa inay joogaan.
- M - Monoklonal gammopathy ama monoclonal plasma proliferative disorder, oo labadaba micnaheedu yahay unugyada unugyada unugyada aan caadiga ahayn
- S - maqaarku waa isbeddelaa sida korodhka maqaarka oo kor u kacay (hyperpigmentation); korodhka timaha (hypertrichosis) ee wejiga, addimada, iyo xabadka; maqaarka oo adkeynaya iyo adkayn, barar (barar) lugaha iyo cagaha, cadeynaya ciddiyaha.
Shakhsiyaadka ayaa sidoo kale laga yaabaa inay dareemaan, daal, jirro xanuun iyo xanuun, ama isbeddelka aragga, calaamadaha kale.
Ciladeynta
Calaamadaha cudurka 'POEMS syndrome' waxaa laga yaabaa in lagu sameeyo baaritaanka jireed ee bukaanka iyo taariikhdiisa caafimaad. Imtixaanka dhiigga sida unugyada dhiigga ee buuxa (CBC) iyo immunoelectrophoresis protein ayaa la sameeyaa si loo eego isbeddellada, sida baaritaanka kaadida. Heerarka hoormoonada qanjirka, heerarka gulukooska dhiigga, iyo heerarka estrogen ee dhiigga ayaa la tijaabiyaa si loo ogaado cilladaha aan caadiga ahayn.
Dhaawaca lafaha lafaha iyo / ama lafaha raajo ayaa loo samayn karaa si loogu caawiyo baarista.
Qofka waxaa loo tixgeliyaa inuu qabo cudurka 'POEMS syndrome' haddii 'P' (polyneuropathy) iyo 'M' (unugyada dhiigga aan caadiga ahayn) ay la socdaan nabarada lafaha (scarring) lafaha ama cudurka Castleman. Dad badan ayaa leh astaamaha kale ee cudurka. Sababtoo ah dhakhaatiir badani ma yaqaanaan cudurka POEMS syndrome, natiijooyinka baaritaanka aan caadiga ahayn ee baaritaanka dhiigga badiyaa waxay keenaysaa khalad-darro ah mellomaayada badan, ama calaamadaha polyneopathy waxay horseedi karaan khalad ah dabaysha "polyneuropathy" (CIDP).
Daaweynta
Daaweynta POEMS syndrome waxay ku xiran tahay daaweynta cudurka unugyada dhiigga ee hooseeya. Dadka intooda ugu badan waxay helayaan daaweyn isku dhafan sida:
- Daweynta shucaaca
- Dawooyinka Corticosteroid sida prednisone
- Chemotherapy
- Hormone beddelidda hormoonnada oo aad u hooseeya
- Daawaynta jirka
- Dhaqtarka lafdhabarta
Khabiirada takhasuska leh sida dhakhtarka neerfaha (dhakhtarka habdhiska dareenka), kalkaaliye caafimaad (dhakhtarka cudurada dhiiga), dhakhtarka maqaarka (dhakhtarka maqaarka), iyo endocrinologist (dhakhtar hormoon ah) ayaa badanaa ku lug leh daryeelka qofka qaba cudurka POEMS.
Ilaha:
Dispenzieri, Angela. "POEMS Syndrome." Hematology 2005 (2005): 360-367.
Dirk R. Larson, Philip R. Greipp, Thomas E. Witzig, Rita Basu, Guillermo A. Suarez, Rafael Fonseca, David Beckham, Danny Welbeck, Marcela Q., Martha Q. Lacy, S. Vincent Rajkumar, Terry M. Therneau, Dirk R. Larson, John A. Lust, & Morie A. Gertz. "POEMS syndrome: qeexitaannada iyo natiijada muddada dheer." Dhiiga 101 (2003): 2496-2506.
"Calaamadaha cudurka POEMS." Daaweynta Cudurka POEMS ee Mayo Clinic. Mayo Clinic. 22 Maajo 2007
Chan, Joanna, & Wingfield Rehmus. "POEMS Syndrome." eMedicine. 15 Dec 2006. WebMD. 22 Maajo 2007