Kaalmada Daawada Kale Iskuday Maareynta Musqusha Musqusha?

Doorashooyinka kale ee khatarta yar ee khatarta ah ayaa laga yaabaa inay sameeyaan isbeddel fiican

Dumarka musqulaha waa nooc ka mid ah xanuunada jimicsiga hidde-wade ee lagu calaamadeeyey daciifnimada horumarka, leexinta, iyo kacsanaanta muruqyada qalfoofka ee xakameynaya dhaqdhaqaaqa. Ma jirto daawo loo yaqaan 'dystrophy', oo bukaanku marar badan ayay u rogtaan dawooyin kale si ay uga caawiyaan daaweynta cudurka.

Waxyaabaha Dabiiciga ah ee Musqusha loo yaqaan 'Muscular Dystrophy'

Ilaa hadda, daraasado yar ayaa tijaabiyay isticmaalka daawada kale ee daaweynta dystrophy muruqa .

Si kastaba ha ahaatee, waxaa jira caddayn ah in noocyada daawooyinka kale ee daawooyinka kale ay bixin karaan faa'iidooyinka qaar bukaanka musqulaha ah, inkastoo inta badan daraasaduhu sii weynaanayaan. Halkan waxaa ku xusan dhowr natiijooyin waxbarasho oo muhiim ah:

1) Qalabka Cuntada

Qaar ka mid ah daraasado yar ayaa muujinaya in dheef-shiid kiimikaadka uu ka faa'iideysan karo bukaanka musqusha. Tusaale ahaan, 2006 daraasaddan oo ka soo baxday 'Journal of American Nutrition Clinical' ayaa lagu ogaaday in la kordhiyo dheecaanka amino acids ay ka caawisay in la joojiyo aaladda jirka ee jirka oo dhan (habdhaqanka Duchenne muscular dystrophy). Daraasaddu waxay ku lug lahayd 26 wiil oo leh duchensne muruqa duxstrophy, mid kasta oo ka mid ah ayaa lagu daaweeyay cusbitaalada amino acid muddo 10 maalmood ah.

Cilmi-baaris horudhac ah ayaa sidoo kale muujinaysa in abuuraha (amino acid oo gacan ka geysanaya in unugyada muruqyada leh tamar) ay ka caawiso daaweynta dystrophy murqaha sidoo kale. Si kastaba ha ahaatee, 2005-tii cilmi-baarista ah ee 50 wiilasha leh Duchenne dystrophy (oo lagu daabacay Annals of Neurology ), saynisyahannadu waxay arkeen in lix bilood oo daaweyn ah oo la socota dabiiciga loo yaqaan 'creatine supplements' ay ku guul darreysteen inay kor u qaadaan awoodda muruqyada ee ka qaybgalayaasha.

2) Qigong

Qigong waxay kor u qaadi kartaa fayoobida dadka qaba murqaha musqusha, sida laga soo xigtay cilmi baaris 2004 ah oo lagu daabacay Disability and Rehabilitation. Daraasadu waxay ku lug laheyd 28 bukaan oo qaba muruqa muruqa, qaar ka mid ah waxay sheegeen in ay hagaajinayaan fayoobida maskaxda, jirka iyo nafsaaniga ah (marka lagu daro hoos u dhigga heerarka walbahaarka) ka dib markii la cuno qigong.

3) Shaaha Cagaaran

Cilmi-baaris ku samaysay jadeecada, cilmi-baarayaashu waxay ogaadeen in epigallocatechin gallate (antioxidant laga helay shaaha cagaaran) laga yaabo in ay ka faa'iidaystaan ​​dadka qaba dufka Duchenne, sida lagu sheegay cilmi-baaris horudhac ah oo lagu daabacay "Journal of Physiology" waxay ka caawisaa sidii looga hortagi lahaa murqaha murqaha oo ay keento muruqyada muruqyada. Si kastaba ha ahaatee, waa wax aad u yar in la sheego in haddii shaaha cagaaran uu saameyn isku mid ah ku yeelan karo bini-aadanka.

Foomamka Dystrophy Muscular

Waxaa jira in ka badan 30 cudur oo lagu sifeeyo dystrophy muruqa. Inkasta oo qaababka qaarkood ay u muuqdaan kuwa yar yar ama carruurnimada, kuwa kale lama arki karo ilaa da'da dhexe ama dambe ee nolosha. Calaamadaha sida da'da bilawga ah, heerka maskaxda daciifka ah, iyo xaddiga socodsiintu waxay ku xiran tahay qaabka muruqyada muruqyada.

Nooca ugu caansan ee muruqyada muruqyada waxaa loo yaqaan 'Duchenne dystrophy'. Caadi ahaan saamaynta wiilasha, Duchenne dystrophy waxaa sababa maqnaanshaha dystrofin (borotiinka oo kaalin weyn ka ciyaaraya ilaalinta sharafta muruqa). Dystrophy muruqa duxstrophy ayaa caadi ahaan u muuqda inta u dhexeysa seddex ilaa shan sano, inta badan dadka buka oo aan awoodin inay ku socdaan da'da 12 jirka.

Noocyada kale ee muruqyada muruqyada waxaa ka mid ah muruqyada muruqyada maskaxda (waxaa lagu tilmaamaa daciifnimo horumarin ah muruqyada wajiga, gacmaha, lugaha, iyo wareega garabka iyo laabta) iyo calaamadaha muruqyada myotonic (oo lagu gartey muruqyada muruqyada dheeraadka ah, cataracts, isbedelka wadnaha, iyo dhibaatooyinka endocrine ).

Calaamadaha iyo Calaamadaha Murqaha Musqusha

Astaamaha iyo calaamadaha muruqyada muruqyada waxay ku kala duwan yihiin qaabka muruqyada murqaha. Tusaale ahaan, calaamadaha iyo calaamadaha Duchenne dystrophy waxaa ku jiri kara dhaqdhaqaaqa gaaban, hoos u dhaca, daciifnimada xudduudaha hoose, muruqyada kubbada iyo garashada garaadka. Daawada muruqyada ee Myotonic, ayaa waxay sababi kartaa calaamadaha sida daciifnimada muruqyada wajiga (iyo sidoo kale gacmaha iyo lugaha iyo muruqyada saameynaya hadalka iyo liqitaanka), xiirto, dhibaatooyinka neefta, iyo cilladaha wadnaha ee waayeelka hore.

Daaweynta Musqusha

Daaweynta musqusha waxaa inta badan ka mid ah daaweynta jirka, daaweynta neefsiga , daaweynta hadalka , qalabka orthopedic loo isticmaalo taageerada, iyo qalitaanka orthopedic corrective.

Daawooyinka qaarkood ayaa sidoo kale loo isticmaalaa in lagu daaweeyo xuubka murqaha, oo ay ku jiraan corticosteroids (si loo yareeyo murqaha musqusha), anticonvulsants (si loo xakameeyo suuxdinta iyo dhaqdhaqaaqa muruqyada), difaaca jirka (si loo yareeyo waxyeelada dhimashada unugyada muruqyada), iyo antibiotics (si loola dagaallamo caabuqyada neefsashada) .

Xaaladaha qaarkood, musqulaha muruqyada bukaanka ayaa laga yaabaa inay u baahan yihiin hawo caawimaad leh (si loo daaweeyo daciifnimada muruqyada neefsashada) iyo / ama qalabka wadnaha (si loo daweeyo isbeddelka wadnaha).

Isticmaalidda Daawada Kale ee Mushaarada Musqusha

Haddii aad ka fekereyso isticmaalka nooc kasta oo daaweyn kale ah daaweynta xanuunka muruqyada, waxaa muhiim ah in lala xiriiro takhtarkaaga (ama dhakhtarka ilmahaaga) ka hor inta aan la bilaabin daaweynta. Daawooyinka murqaha oo isdabamarin leh daaweyn kale iyo ka fogaansho ama dib u dhigida daryeelka caadiga ah waxay yeelan karaan cawaaqib xun.

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