Ciladda Nidaamka Neerka Nadaafadeed Caadi ahaan badanaa loogu talagalay Parkinson
Nidaamyo badan oo kala duwan (MSA) waa cudur taasoo keenta qaybo badan oo ka mid ah nidaamka dareenka si ay u kacaan. MSA waxay ka kooban tahay seddex syndrome: shy-drager syndrome, xummad diidmo-darro, iyo olivopontocerebellar atrophy. MSA waa cudur sii socda oo saameeya nidaamka dareenka madaxbannaan, qeyb ka mid ah jirkaaga oo xakameynaya falalka miyir-qabka ah sida dheef-shiidka iyo neefsashada.
MSA waxay saameysaa meel kasta oo ka timid laba illaa 15 qof 100,000 oo qof. Waxay qaadan kartaa mudo ah in la helo ogaanshaha MSA sababta oo ah isbeddelada udhexeeya MSA iyo xaalado kale, sida cudurka Parkinson . MSA waxaa badanaa laga helaa qiyaastii 50 sano jir waxaana lagu arkaa dadka asal ahaan ka soo jeeda. Marka uu calaamaduhu bilowdo, cudurku wuxuu u eg yahay inuu si degdeg ah u socdo.
Astaamaha Nidaamka Fudud (Multiple System Atrophy)
Calaamadaha MSA waxay ka yimaadaan luminta unugyada dareemayaasha ee nidaamka dareenka. Maxaa keena luminta unugyada dareemayaasha weli aan la aqoon. Dad badan oo leh MSA ogeysiis hore ah sida xasaasiyadda kaadi-celinta, kaadi-galis la'aanta ragga, waxay hoos u dhigtaa cadaadiska dhiigga marka ay taagan yihiin (qalafsanaanta dhiigga), suuxdin, iyo caloosha. Marka ay calaamaduhu horumarayaan, waxay caadi ahaan hoos ugu dhacaan mid ka mid ah laba kooxood:
- Nooca Parkinsonian (MSA-P): tan waxaa ka mid ah calaamadaha la midka ah cudurka Parkinson sida cirib-tirka nasashada, murqaha muruqyada, iyo socodka gaabis
- Nooca nooca Cerebellar (MSA-C): waxay ku lug leedahay socodka (ataxia), dhibaatooyinka ku haya dheelitirka, iyo dhibaatooyinka isku-dubaridka dhaqdhaqaaqa ikhtiyaariga ah.
Calaamadaha kale ee la xidhiidha MSA waxaa ka mid ah dhibaato hadalka ama liqidda, apnea hurdo, iyo gacmo qabow. Dadka qaarkiis ayaa sidoo kale laga yaabaa inay yeeshaan muruqa hurdada, murqaha iyo tendon yaraanta, Pisa syndrome - halkaasoo jidhku u muuqdo inuu ku tiirsan yahay dhinac dhinac ah, taahid la'aan, iyo antecollis - taas oo dhacda marka qoortu ay horay u socoto oo madaxu hoos u dhaco.
Sidee MSA Looga Helay?
Waxay noqon kartaa mid aad u adag in la kala saaro MSA laga bilaabo cudurka Parkinson . Mid ka mid ah habka loo kala saaro labadaba waa in la eego sida ugu dhakhsaha badan cudurku u socdo. MSA waxay u egtahay in ay si dhakhso ah u horumarto marka laga reebo Parkinson. Dad badan oo qaba MSA waxay u baahan yihiin qalab gargaar ah, sida kursiga curyaamiinta ama bakoorad, dhawr sano gudahood markii la ogaado.
Siyaabo kale oo loo kala saaro labadaba waa in lagu daaweeyo Parkinson. MSA si fiican ugama jawaabin levodopa, daawada loo isticmaalo daaweynta Parkinson. Nasiib darro, qanjiraha ayaa ah sida keliya ee lagu ogaan karo MSA. Imtixaanka takhasuska leh, sida baaritaanka PET-ka (sawir-shaxanka xasaasiyadda positron-ka), ayaa ka saari kara noocyada kale ee xanuunka niyolojiga dhifka ah.
Daaweynta MSA
Waqtigaan, ma jirto wax daawo ah ee MSA, mana jirto wax daaweyn ah oo loogu talagalay in lagu celiyo ama joojiyo horumarka cudurka. Qaar ka mid ah xaaladaha cudurka ayaa ah mid dhib badan oo dhib badan. Xanuunka dhaqdhaqaaqa waxaa lagu daaweyn karaa levodopa iyo carbidopa (Sinemet), laakiin tani badanaaba waxay leedahay natiijooyin kooban.
Daawooyinka kale sida "bromocriptine" (Parlodel), trihexyphenidyl (Artane), mestrate (Cogentin), iyo amantadine (Symmetrel), ayaa sidoo kale ku siin kara calaamadaha qaarkood.
Daweynta jirka, oo ay ku jirto daaweynta aqua, waxay gacan ka geysan kartaa sii socodka muruqyada, iyo daaweynta hadalka ayaa gacan ka geysan karta hagaajinta wixii dhibaato ah ee liqa ama hadalka.
Cilmi-baaristu waxay sheegaysaa
Wax yar ayaa laga ogyahay hababka shaqada ee nidaamyada kala duwan. Cilmi-baareyaasha ka socda Machadka Qaran ee Dhibaatooyinka Nuuroole iyo Stroke (NINDS) ayaa hadda isku dayaya inay ogaadaan sababta borotiinka alpha-synucleinin ay ku sameysmaan unugyada glyal (unugyada difaaca nuuroonada nidaamka dareemayaasha) ee dadka qaba MSA iyo neuronal (dareemayaasha) unugyada dadka qaba cudurka Parkinson. Maxkamad caafimaad ayaa isku dayday isticmaalka rifampicin daroogada si loo yareeyo horumarka cudurka, laakiin daaweyntu waxay ahayd mid aan waxtar lahayn.
Xogta laga helay daraasaddan hadda waxaa loo isticmaalaa daraasadaha kale ee MSA.
Ilaha
Diedrich, A., & Robertson, D. (2002). Nidaamyo badan oo kala duwan. eMedicine, oo laga heli karo http://www.emedicine.com/neuro/topic671.htm
Machadka Qaran ee Cudurrada Dareemaha iyo Istaroogga. Xaanshida Xaqiiqada ee Fudud (Atrophy Fact Sheet). Noofembar 2014.