Cudurka Sheroid-Dareenka ah ee La-qabsashada Is-Wareegga W / Autoimmune Thyroiditis
Cudurka loo yaqaan " Hashimoto's Encephalopathy " ayaa markii ugu horraysay lagu sharraxay 1966-kii. Ka dib wakhtigaas, dhakhaatiirtu waxay bilaabeen inay soo uruuriyaan warbixinnada kiisaska, "Hashimoto Encephalopathy" waxay noqotay magaca la aqoonsan yahay ee xaaladaha cudurka encephalopathy ee la xidhiidha thyroiditis ee Hashimoto.
Sababtoo ah bukaanka badankooda Hashimoto ee Encephalopathy waxay sii wanaajiyaan daaweynta steroids ama daaweynta difaaca jirka, khabiiro qaar ayaa hadda tixraacaya xaaladda sida "ensterfalopathy-macmacaanka ah ee la xidhiidha thyroiditis" (SREAT).
Xaaladaha qaarkood, xaaladdu waxaa kale oo loo yaqaan "" non-xinjirjabdhiska miyir-dareenka 'meningoencephalitis "(NAIM), oo ay ku jiri karto oo kaliya dhibaatooyinka tayroodhka ah ee cusbataallada, laakiin sidoo kale xanuunada kale ee isbitaallada sida Sjögren syndrome iyo lupus erythematosus-xiriirka meningoencephalitis. Caadooyinka guud ee dhammaan xaaladahan waa inay ka jawaabaan daaweynta steroid.
Ereyga "encephalopathy" waxaa loola jeedaa cudur maskaxda ah oo bedelaaya maskaxda ama dhismaha. Muuqaalka muhiimka ah ee encephalopathy-ga waa isbeddel maskaxeed. In kastoo ay calaamaduhu ku xiran yihiin nooca cudurka encephalopathy iyo sida uu u daran yahay, astaamaha caadiga ah waxaa ka mid ah:
- xusuusin la'aan
- Dhibaatada xoogga leh
- lumitaanka awoodda fahamka iyo shaqada
- isbedel shakhsiyadeed
- murugo iyo daal
- miyir beelid
- myoclonus (murqaha aan khasab ahayn ee muruqyada)
- nystagmus (dhaqdhaqaaq isha oo degdeg ah, aan is-qabad lahayn)
- tufaax
- daciifinta muruqyada
- waallida
- qalalaasaha, qalalaasaha
- liqidda dhibaatada
- dhibaatada hadalka
Astaamaha kale ee la arki karo waxaa ka mid ah:
- jahawareer, jaahwareer
- maskaxda
- madax xanuun
- haemortesis - dhinaca midig ee curyaan ah
- Dhibaatooyinka dhaqdhaqaaqa dhaqdhaqaaqa - dhibaatooyinka isku xirka gacmaha, gacmaha, faraha
Sababtoo ah Hashimoto Encephalopathy / SREAT ayaa si khalad ah u fahamsan, baadhitaan ay soo saartey Febraayo 2006 Archives of Neurology , khubaro waxay soo bandhigeen inay tilmaamayaan natiijooyinka kala duwan ee kiliinikada, sheybaarka, iyo raadiyeyaasha shucaaca ee xaaladda.
Hadafkoodu waa inay ka caawiyaan hagaajinta awoodda dhakhaatiirta si ay u aqoonsadaan ugana baaraan xaaladdan.
Daraasadu waxay eegtey 20 bukaan (14 haween, 6 rag ah) kuwaas oo laga helay 1995 ilaa 2003. Da'da dhexdhexaadka ah ee cudurka bilawga ah waxay ahaayeen 56 sano, oo leh qiyaas ahaan 27 illaa 84 sano (kala duwan, 27-84 sano).
Tilmaamaha daaweynta / astaamaha ugu badan ee la daaweyn karo waxay ahaayeen:
- Cadaadiska - 80%
- Afka-socodka 'Transcasia' - 80% (Aphrasia waa ku adag tahay luqadda, saamayn ku yeelashada kartida hadalka, akhriska ama qorista)
- Myoclonus - 65% (isku-dhafid, qasab la'aan muruqa ama koox muruq ah)
- Gait ataxia - 65% (socod aan xiirin ama is-xajin, socodka adag)
- Qalalaasaha - 60%
- Dhibaatooyinka hurdada - 55%
Misdiagnnimadu waa Standard
Waa maxay walwal gaar ah waa in khubarada ay ogaadeen in BUKAANKA DHAMMAAN asal ahaantii la ogaaday. Tusaale ahaan:
- Cudurka fayraska Viral - 25%,
- Jahawareerka Is-beddelka - 20%
- Cudurka Creutzfeldt-Jakob - 15% (Cudurka Creutzfeldt-Jakob waa cudur naadir ah oo aan caadi ahayn, oo maskaxda ka dilaacda, mararka qaarkood si qalad ah ayaa loo yaqaan "Cow Cow Cudurka"
Shaybaarada iyo baaritaannada aan caadiga ahayn ee Hashimoto Encephalopathy / SREAT
Tiro badan oo ah baaritaano ayaa la arkay, oo ay ka mid yihiin:
- Heerarka enzymes-kordhay - 55%
- Heerarka hormoonada ee kor u kaca ee hormoonada (TSH) - 55%
- Heerka sare ee foosha ee "lime" ("sicir dhimis") - 25%
- Xasaasiyadda dareeraha ee Cerebrospinal oo soo jeedinaysa barar - 25%
- Cudurka sawir-maskaxeed ee Magnetic-ka ee Isku-dhafan ee la socota encephalopathy - 26%
Gabagabo
Cilmi baarayaashu waxay ku soo gabagaboobeen in ay jiraan waxyaabo kala duwan oo ka mid ah natiijooyinka la xidhiidha Hashimoto Encephalopathy / SREAT, iyo in khaladku yahay mid caadi ah.
Cilmi baarayaashu waxay ku talinayaan in Hashimoto Encephalopathy / SREAT waa in la tixgeliyaa xitaa haddii TSH iyo "sicir dhimis" ay caadi yihiin, dheecaanka cerebrospinal ma muujiyo caddaynta caabuqa iyo MRI waa caadi.
Macluumaad Dheeraad ah
Hashimoto Bogga Macluumaadka Ensefalopathy
> Isha
> Castillo, Pablo MD; et. al. "Steroid-Responsive Encephalopathy Associated oo leh Otogaamin Automayts." Arch Neurol . 2006; 63: 197-202. (Qeybta 63-aad, 2-aad, Febraayo 2006)
> Machadka Qaran ee Cudurrada Dhimirka iyo Istaroogga