Qeexitaan, Astaamaha Lifatarta Mantle Cell
Maxay tahay lymphoma unugyada, iyo maxaan ka ogaanayaa noocyadan kansarka ah?
Guudmarka
Mantle Cell Lymphoma waa nooc aan caadi ahayn ee lymphoma (NHL) . Kaliya 5-7% dhammaan kooxaha NHL waxay ka tirsan yihiin kooxdan. Waa lymfoma of B lymphocytes, ama "B-unugyada." Inkastoo ay u egtahay qanjirro qunyar-socod ah, bukaanka hoose-hoose ee yar yar ee mikroskoobka, badanaa wuu sii koraa oo u dhaqmaa sida lymphoma-ka sareeya.
Waxaa loogu yeeraa 'lafaarta' unugyada 'mantle' sababta oo ah waxay marka hore ka soo baxdaa qeyb ka mid ah naqshadda limfiga oo loo yaqaan 'mantle'.
Waxyaabaha Halista ah
Mantle Cell Lymphoma wuxuu ku badan yahay ragga marka loo eego dumarka iyo dadka waayeelka ah. Da'da da'da ee cudurka lagu ogaado waa in ka badan 60 sano. Ma jiraan wax calaamado ah oo halis ah oo lagu heli karo nooca lenfoma, inkastoo ay jiraan waxyaabo badan oo ka yimaada infekshannada illaa kiimikada ayaa loo eegay sida ugu macquulsan ee halista lymfoma ee non-Hodgkin's lymphoma guud ahaan.
Astaamaha
Lymphoma mantle cell wuxuu ka bilaabmaa qanjaha lafaha. Waxa ugu horreeya ee dadka badankood wax ka ogaadaan waa noodaha qoorta ee qoorta, gumaarka ama kilkisha. Cudurku guud ahaan wuu sii koraa, wakhtigana uu dhakhtarku arko, cudurku wuxuu ku faafaa xubnaha kale ee jidhka. Dadka qaarkiis cudurku waa gaabis sii kordhaya, waxyaallaha kansarku waxay u tixraacaan sida "indolent" laakiin taasi waa ka reeban tahay. Dhaawaca lafaha, beeryarada, dhuunta naadirku waxay ku dhacdaa dad badan, waxaana jira inta badan unugyada lymphoma ee dhiiga.
Xiidmaha ayaa sidoo kale saameyn kara dadka qaarkood, waxayna keenaan calaamadaha sida xanuunka caloosha ama shubanka.
Ciladeynta
Tijaabooyinka loogu talagalay laf-dhabarka unugyada Mantle-du waa kuwa la mid ah noocyada kale ee lymfoma. Waxaa ka mid ah baaritaano dhiig, baaritaan iyo baaritaanka dhuuxa lafta . Marka baaritaanku muujiyo qaybo ka mid ah jirka ayaa la saameeyaa, marxaladda cudurka ayaa la go'aamin karaa .
Dadka intooda ugu badan waxay qabaan xanuunka heerka III ama IV ee ku faafay xubnaha jidhka ee kala duwan.
Daaweynta
Lymphoma mantle cell badanaa waxaa lagu daaweeyaa daaweynta kiimikada, laakiin sida aadka ah loo daweeyo waxaa ay ku xiran tahay da'da. Dhalinyarada, dadka waaweyn ee caafimaadka qaba, kiimiko daaweyn oo ay raacdo qalliinka unugga unugyada ayaa laga yaabaa inuu noqdo ikhtiyaar wanaagsan, laakiin wuxuu keenaa sunta weyn. Daaweynta waa wax aan caadi ahayn haddii cudurku hore loo ogaado, iyo ujeeddada daaweyntu waa inuu ilaaliyo cudurka xakamaynta ilaa inta suurogal ah. Daaweynta intooda badani waxay isugu jiraan Rituxan (rituximab) waxaana daawadan loo isticmaali karaa dayactirka daaweynta ka dib.
Daawooyinka cusub sida Velcade (bortezomib) iyo Treanda (bendamustine) ayaa ah kuwa lagu badalo hababka kiimikada. Daawooyin badan oo kala duwan oo daroogo iyo daawooyin cusub ayaa lagu bartaa tijaabooyinka bukaan socodka, waxaana suurtagal ah in daaweyn cusub iyo daaweyn cusub oo loogu talagalay lafdhabarka loo yaqaan 'mantle cell lymphomawill' mustaqbalka dhow.
Maadaama cudurka badankood uu sarreeyo, daaweynta sida qalitaanka iyo daaweynta shucaaca inta badan waxay leeyihiin door la xaddidan.
La qabsashada
La qabsashada cudurka cusub ee lymphoma waxay noqon kartaa wax burburin kara. Xagee ka billaabataa marka ugu horeysa ee lagaa baaro? Dadka qaarkood, daaweynta gardarrada ah waxay noqon kartaa ikhtiyaarka ugu fiican.
Dadka kale, daaweynta gardarrada ah maaha inay noqoto doorashada ugu fiican. Hase yeeshee, weli waxaa jira rajo ah in tayo wanaagsan oo nolol leh waqtiga aad haysato. Fiiri talooyinkaan ku saabsan qaadashada kansarka dhimirka . U gee qoyskaaga iyo saaxiibbada . Waxaa jira jaaliyad taageero weyn oo dadka qaba lymphomas online oo loogu talagalay kuwa doonaya taageerada kuwa kale ee la mid ah wax la mid ah. Xusuusnow in cilmi-baaristu socoto, iyo in ay jiraan horumar aad u balaadhan oo ka socda daaweynta kansarka maanta.
Ilaha:
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Dreyling, M., Ferrero, S., iyo Network Mantle Cell Lymphoma Network. Doorka daaweynta la beegsanayo ee laf-dhabarka unugyada jirka: waa meydaan dhintay mise noolaan? Haematologica . 2016. 101 (2): 104-14.
Lunning, M., iyo J. Armitage. Goobta loo yaqaan 'transplantation in lymphoma'. Oncology . 2013. 27 Qalabka 2: 2-6.
Maddocks, K., iyo K. Blum. Xeeladaha daaweynta ee lenfomada naqshada. Daaweynta Kansarka iyo Cilmi-baarista . 2015. 165: 251-70.
Martin, P. Ibrutinib - daaweyn cusub oo loogu talagalay lymphoma mantarka laf-dhabarka? Lancet . 2015 Dec. (Epub ka hor daabac).
Tucker, D., iyo Qaanuunka S. Ibrutinib oo loogu talagalay lymphoma mantle cell. Future Oncology . 2016. 12 (4): 477-91.
Vose, J. Mantle lymphoma: 2015 cusbooneysiinta ku saabsan ogaanshaha, halis-halis, iyo maareynta daaweynta. Somali Journal of Hematology . 2015. 90 (8): 739-45.